Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)

Definition

Definition of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Pulmonary hypoplasia or aplasia is part of the spectrum of malformations characterized by incomplete development of lung tissue. The severity of the lesion depends on the timing of the insult in relation to the stage of lung development and the presence of other anatomic anomalies. The hypoplastic lung consists of a carina, a malformed bronchial stump, and absent or poorly differentiated distal lung tissue.

Symptoms

Symptoms of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Lung Hypoplasia Leading To Respiratory Problems, Growth Retardation, Midfacial Hemangioma, Facial And Jaw Deformities, Respiratory Problems, And Abdominal Hernias. Cognition And Speech Are Usually Normal

Causes

Causes of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Pulmonary hypoplasia may be primary, but it is usually secondary, manifested by small fetal thoracic volume caused by compression in the hemithorax due to structures such as abdominal contents in CDH or congenital anomalies such as CAM or cysts.

Diagnosis

Diagnosis of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
The external chest may appear normal or may be small and bell shaped, with or without scoliosis. A mediastinal shift is observed toward the involved side, and dullness upon percussion is heard over the displaced heart. In right-sided hypoplasia, the heart is displaced to the right, which may lead to a mistaken diagnosis of dextrocardia. Breath sounds may be decreased or absent on the side of hypoplasia, especially over the bases and axilla.

Treatment

Treatment of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Consult with your doctor.

Prognosis

Prognosis of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Consult with your doctor.

Prevention

Prevention of Arthrogryposis (Multiplex Congenita Pulmonary Hypoplasia)
Consult with your doctor.