This condition is a rare association of profound thrombocytopenia associated with two rare vascular tumors: kaposiform hemangioendotheliomas and tufted angiomas.

Symptoms

Purpura,Skin hemorrhage,Abnorma lbleeding,Bleeding from gums,Large capillary angioma,Hemorrhagic skin spots,Bruises,Low blood platelet level,Anemia,Hypofibrinogenemia

Diagnosis

This is diagnosed by blood counts, clotting studies, ultrasound, CT scan, MRI,.

Treatment

corticosteroids,alpha-interferon,chemotherapy ,radiation therapy are used to cure this disorder.